progressive familial intrahepatic cholestasis (Q1018534)
intrahepatic cholestasis characterized by early onset of chronic unremitting cholestasis of hepatocellular origin that progresses to hepatic fibrosis, cirrhosis, and end-stage liver disease before adulthood
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aliases PFIC
 Byler disease
description intrahepatic cholestasis characterized by early onset of chronic unremitting cholestasis of hepatocellular origin that progresses to hepatic fibrosis, cirrhosis, and end-stage liver disease before adulthood

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(P699) DOID:0070221
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(P7464) progressive-familial-intrahepatic-cholestasis
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(P11143) Progressive familial intrahepatic cholestasis